Total anomalous pulmonary venous connection of the infracardiac variety: An unusual congenital defect in neonatology

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Viviana Elizabeth Belduma Belduma
Andrea Mariana Meza Zambrano
Alex Javier Villalta Herrera

Abstract

Total anomalous pulmonary venous connection (TAPVC) is a congenital heart defect that represents less than 1.5% of children born with any heart defect, with a poor prognosis for those who do not undergo timely surgical correction. A case is presented of a male neonate, 2 days old, who was admitted with a clinical picture of respiratory failure requiring mechanical ventilation. After further studies, he was diagnosed with TAPVC, followed by corrective surgery, a torpid evolution, and death at 14 days of life. The objective of this report is to illustrate the management and clinical presentation of an infrequent pathology, which also corresponds to an unusual variety.

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How to Cite
Belduma Belduma, V. E., Meza Zambrano, A. M., & Villalta Herrera, A. J. (2026). Total anomalous pulmonary venous connection of the infracardiac variety: An unusual congenital defect in neonatology. Revista Ecuatoriana De Pediatría, 27(1), 72–76. https://doi.org/10.52011/RevSepEc/e353
Section
Clinical Case
Author Biographies

Viviana Elizabeth Belduma Belduma, Universidad Católica Santiago de Guayaquil - Hospital Roberto Gilbert Elizalde

Médicos Posgradistas de Pediatría, Universidad Católica Santiago de Guayaquil, Hospital Roberto Gilbert Elizalde, Guayaquil – Ecuador

Andrea Mariana Meza Zambrano, Universidad Católica Santiago de Guayaquil - Hospital Roberto Gilbert Elizalde

Médicos Posgradistas de Pediatría, Universidad Católica Santiago de Guayaquil, Hospital Roberto Gilbert Elizalde, Guayaquil – Ecuador

Alex Javier Villalta Herrera, Hospital Roberto Gilbert Elizalde

Imagenólogo Pediatra, Hospital Roberto Gilbert Elizalde, Guayaquil – Ecuador

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